Author: Stephanie Grant, MD – Emory University and Children’s Healthcare of Atlanta


A three-week-old female with supravalvular aortic stenosis, peripheral pulmonary artery stenosis, and dysmorphic facial features consistent with an elfin-like face is being evaluated prior to supravalvular aortic stenosis repair. A transthoracic echocardiograph demonstrates narrowing of the aorta at the sinotubular junction with a supravalvular aortic gradient of 90 mmHg and normal coronary arteries. Results of genetic testing are pending. Which of the following electrolyte abnormalities would you MOST LIKELY expect on this patient’s pre-operative labs?