Author: Michael A. Evans, MD – Ann & Robert H. Lurie Children’s Hospital of Chicago, Northwestern Feinberg School of Medicine


A 1-hour old neonate presents with persistent cyanosis. Prostaglandin E₁ is initiated via an umbilical venous line. The differential diagnosis includes Tetralogy of Fallot and work up is initiated with a transthoracic echocardiogram (TTE) and computed tomography (CT) of the chest. Which of the following anomalies associated with Tetralogy of Fallot is MOST LIKELY present in this neonate?