Author: Anna Hartzog MD and Chinwe Unegbu MD – Children’s National Hospital


A 14-year-old male adolescent patient with severe idiopathic pulmonary hypertension presents for right heart catheterization. As compared to a similar aged patient with repaired Tetralogy of Fallot and residual severe pulmonary valve stenosis, which echocardiographic feature MOST ACCURATELY describes the adaptation of the right ventricle in this patient with idiopathic pulmonary hypertension?